Pulmonary Hypertension in Congenital Heart Disease
Published: June 26, 2023
- Pulmonary hypertension (PH) associated with congenital heart disease is an increasingly common cause of PH. The improvements in diagnosis and management of CHD have led to increased survival into adulthood accompanied by a significant number of associated cardiac sequelae, including PH. However, data guiding management of this form of PH are limited.
- The prognosis for PH-congenital heart disease is variable and dependent on the type of congenital heart disease and other factors. Evaluation for surgical repair must take the risks associated with the late repair of congenital heart disease into account when intervention is considered.
- A collaborative, multi-disciplinary approach involving cardiologists, PH subspecialty care teams, and cardiothoracic surgeons in partnership with patients and families is key to improving outcomes and quality of life for people with PH-congenital heart disease.
Supporting Materials
- Commentary: It's Classified: The Complexity of Pulmonary Hypertension Associated with Congenital Heart Disease by Catherine M. Avitabile, MD
- Top Things to Know: Pulmonary Hypertension in CHD
Recommended Reading
- 2018 AHA/ACC Guideline for the Management of Adults With Congenital Heart Disease
- Survival in Children With Congenital Heart Disease: Have We Reached a Peak at 97%?
- Lifetime Prevalence of Congenital Heart Disease in the General Population From 2000 to 2010
- Congenital Heart Disease The Remarkable Journey From the “Post-Mortem Room” to Adult Clinics
- ACCF/AHA 2009 Expert Consensus Document on Pulmonary Hypertension
- Changing Landscape of Congenital Heart Disease
- Elucidating the Clinical Implications and Pathophysiology of Pulmonary Hypertension in Heart Failure With Preserved Ejection Fraction