Adult Moyamoya Disease and Syndrome Current Perspectives and Future Directions

Published: August 23, 2023

suzuki digital subtraction angiography
  • Adult moyamoya disease and syndrome is a rare disorder characterized by an abnormal formation of abnormal network of dilated and fragile blood vessels in the brain. It is a heritable disease and carries a significant morbidity and mortality.
  • This disorder is most prevalent in Japan and Asia but is also seen in the United States.
  • This paper updates definitions of moyamoya disease and syndrome and discusses modern methods of diagnosis and updates information on pathophysiology, epidemiology, and medical and surgical treatment.